Système respiratoire

Carte du réseau national

Hypertension pulmonaire

Filière Respifil

Les Missions du centre

  • Assurer une expertise diagnostique
  • Favoriser les actions de prise en charge et proposer un parcours de soins adapté pour les patients et leurs familles

La liste des pathologies concernées par le centre

  • Hypertensions artérielles pulmonaires
  • Hypertensions pulmonaires rares
  • Hypertension thrombo-embolique chronique
  • Hypertension artérielle pulmonaire idiopathique
  • Hypertension artérielle pulmonaire héritable
  • Hypertension artérielle pulmonaire induite par les médicaments et les toxiques
  • Hypertension artérielle pulmonaire associée aux infections par le VIH
  • Hypertension artérielle pulmonaire associée aux cardiopathies congénitales
  • Hypertension pulmonaire associée à l’hypertension portale
  • Hypertension pulmonaire associée aux connectivites
  • Hypertension pulmonaire associée aux anémies hémolytiques
  • Hypertension pulmonaire induite ou associée aux maladies respiratoires et/ou hypoxémies
  • Hypertension pulmonaire d’origine multifactorielle non élucidée


  • Prise de rendez-vous :


  • Pr Nicolas LAMBLIN cardiologue, médecin référent du centre
  • Dr Pascal DE GROOTE, cardiologue
Publications Rang auteurs
Soluble markers of B cell activation suggest a role of B cells in the pathogenesis of systemic sclerosis-associated pulmonary arterial hypertension 1
 Dual-energy CT lung perfusion characteristics in pulmonary arterial hypertension (PAH) and pulmonary veno-occlusive disease and/or pulmonary capillary hemangiomatosis (PVOD/PCH): preliminary experience in 63 patients. DA
 Right heart catheterization in advanced systolic heart failure. What are the most useful haemodynamic parameters for risk stratification? 1
 Pulmonary Arterial Hypertension Associated With Systemic Lupus Erythematosus: Results From the French Pulmonary Hypertension Registry. 1
 Time for precision medicine in systemic sclerosis-associated pulmonary arterial hypertension. 1
 Imaging of pulmonary hypertension in adults: a position paper from the Fleischner Society. 1
 Survival Improved in Patients Aged ≤ 70 Years With Systemic Sclerosis-Associated Pulmonary Arterial Hypertension During the Period 2006 to 2017 in France. 1
Efficacy of immunosuppressants with bridge vasodilator therapy in severe lupus erythematosus-associated pulmonary arterial hypertension 1
 Dual-energy CT (DECT) lung perfusion in pulmonary hypertension: concordance rate with V/Q scintigraphy in diagnosing chronic thromboembolic pulmonary hypertension (CTEPH). DA
 Clinical phenotypes and survival of pre-capillary pulmonary hypertension in systemic sclerosis. 1
 Pulmonary hypertension subtypes associated with hereditary haemorrhagic telangiectasia: Haemodynamic profiles and survival probability. DA
 Pulmonary hypertension in systemic sclerosis: different phenotypes. 1